Primary pigmented nodular adrenocortical disease associated with Carney complex: case report and literature review

CONTEXT: Carney complex (CNC), a familial multiple neoplasm syndrome with dominant autosomal transmission, is characterized by tumors of the heart, skin, endocrine and peripheral nervous system, and also cutaneous lentiginosis. This is a rare syndrome and its main endocrine manifestation, primary pi...

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Bibliographic Details
Main Authors: Fabrícia Torres Gonçalves, Taciana Carla Maia Feibelmann, Cínthia Monteiro Mendes, Maria Luiza Mendonça Pereira Fernandes, Geraldo Henrique Gouvêa de Miranda, Agostinho Pinto Gouvêa, Paulo Tannús Jorge
Format: Article
Language:English
Published: Associação Paulista de Medicina
Series:São Paulo Medical Journal
Subjects:
Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31802006000600007&lng=en&tlng=en