Why, when and how to investigate primary ciliary dyskinesia in adult patients with bronchiectasis

Abstract Bronchiectasis represents the final pathway of several infectious, genetic, immunologic or allergic disorders. Accurate and prompt identification of the underlying cause is a key recommendation of several international guidelines, in order to tailor treatment appropriately. Primary ciliary...

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Bibliographic Details
Main Authors: Martina Contarini, Amelia Shoemark, Jessica Rademacher, Simon Finch, Andrea Gramegna, Michele Gaffuri, Luca Roncoroni, Manuela Seia, Felix C. Ringshausen, Tobias Welte, Francesco Blasi, Stefano Aliberti, James D. Chalmers
Format: Article
Language:English
Published: PAGEPress Publications 2018-08-01
Series:Multidisciplinary Respiratory Medicine
Subjects:
Online Access:http://link.springer.com/article/10.1186/s40248-018-0143-6