Hemophagocytic lymphohistiocytosis and congenital factor VII deficiency: a case report

Abstract Background Hemophagocytic lymfohistiocytosis (HLH) is a rare, life-threatening hyperinflammation, characterized by immune system over-activation resulting in hemophagocytosis. HLH could appear as a primary disease caused by mutations of immune-regulatory genes, or develop as a result of vir...

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Bibliographic Details
Main Authors: Xiong Wang, Ning Tang, Wei Chang, Yanjun Lu, Dengju Li
Format: Article
Language:English
Published: BMC 2018-09-01
Series:BMC Medical Genetics
Subjects:
Online Access:http://link.springer.com/article/10.1186/s12881-018-0673-y