Plasma and fibroblasts of Tangier disease patients are disturbed in transferring phospholipids onto apolipoprotein A-I

Plasmas of patients with Tangier disease (TD) lack lipid-rich α-HDL which, in normal plasma, constitutes the majority of high density lipoprotein (HDL). Residual amounts of apolipoprotein (apo)A-I in TD plasma occur as lipid-poor or even lipid-free preβ-HDL. By contrast to normal plasma, TD plasma d...

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Bibliographic Details
Main Authors: Arnold von Eckardstein, Ali Chirazi, Susanne Schuler-Lüttmann, Michael Walter, John J.P. Kastelein, Jürgen Geisel, José T. Real, Roberto Miccoli, Giorgio Noseda, Gunnar Höbbel, Gerd Assmann
Format: Article
Language:English
Published: Elsevier 1998-05-01
Series:Journal of Lipid Research
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S0022227520338669