Recurrence of emphysema post-lung transplantation in a patient with alpha 1 antitrypsin deficiency (AATD)
The genetic disorder alpha 1 antitrypsin deficiency (AATD) results in reduced levels of alpha 1 antitrypsin (AAT) in the lung and an imbalance between AAT anti-protease activity and the activity of proteases that degrade elastin and connective tissues. This imbalance commonly leads to the excessive...
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Format: | Article |
Language: | English |
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Elsevier
2020-01-01
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Series: | Respiratory Medicine Case Reports |
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Online Access: | http://www.sciencedirect.com/science/article/pii/S2213007120305232 |