Expression of the Tuberous Sclerosis 2 Gene Product, Tuberin, in Adult and Developing Nervous System Tissues

Tuberous sclerosis (TS) is an autosomal dominant disorder in which affected individuals manifest mental retardation, seizures, and a variety of benign and malignant tumors. TheTSC2tumor suppressor gene was recently identified by positional cloning and its protein product, tuberin, shown to represent...

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Bibliographic Details
Main Authors: Robert T. Geist, Anita J. Reddy, Jie Zhang, David H. Gutmann
Format: Article
Language:English
Published: Elsevier 1996-04-01
Series:Neurobiology of Disease
Online Access:http://www.sciencedirect.com/science/article/pii/S096999619690011X