Relapsing granulomatosis with polyangiitis with severe lung and upper respiratory tract involvement successfully treated with rituximab

Granulomatosis with polyangiitis (GPA) is a chronic, relapsing, primary systemic small vessel vasculitis associated with anti-neutrophil cytoplasmic antibodies. The disease is characterised by the involvement of various organs. The relapse rate rises from about 20% at 12 months to about 60% at 5 yea...

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Bibliographic Details
Main Authors: Anna Masiak, Zbigniew Zdrojewski
Format: Article
Language:English
Published: Termedia Publishing House 2017-08-01
Series:Rheumatology
Subjects:
Online Access:https://www.termedia.pl/Relapsing-granulomatosis-with-polyangiitis-with-severe-lung-and-upper-respiratory-tract-involvement-successfully-treated-with-rituximab,18,30511,1,1.html