Case Reports: Emery-Dreifuss Muscular Dystrophy Presenting as a Heart Rhythm Disorders in Children

Emery-Dreifuss muscular dystrophy (EDMD) is inherited muscle dystrophy often accompanied by cardiac abnormalities in the form of supraventricular arrhythmias, conduction defects and sinus node dysfunction. Cardiac phenotype typically arises years after skeletal muscle presentation, though, could be...

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Main Authors: Tatiana Kovalchuk, Elena Yakovleva, Svetlana Fetisova, Tatiana Vershinina, Viktoriya Lebedeva, Tamara Lyubimtseva, Dmitriy Lebedev, Lubov Mitrofanova, Anton Ryzhkov, Polina Sokolnikova, Yuliya Fomicheva, Alexandra Kozyreva, Sergey Zhuk, Natalia Smolina, Anna Zlotina, Tatiana Pervunina, Anna Kostareva, Elena Vasichkina
Format: Article
Language:English
Published: Frontiers Media S.A. 2021-05-01
Series:Frontiers in Cardiovascular Medicine
Subjects:
Online Access:https://www.frontiersin.org/articles/10.3389/fcvm.2021.668231/full