Hyper IgE recurrent infection syndrome in South Asia: is there a different outcome?

Abstract Background Hyper IgE recurrent infection syndrome (HIES) is a rare immune deficiency, characterized by recurrent staphylococcal skin and lung abscesses, pneumonia and increased IgE levels. The majority of autosomal dominant HIES (AD HIGE) is due to hypomorphic mutations in the signal transd...

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Bibliographic Details
Main Authors: Rajiva de Silva, Dhanushka Dasanayake, Manouri Senanayake, Ramya Ediriweera, Savithri Dias, Chandima Karunatilleke, Karen Brocas, Fariba Tahami, Suranjith Seneviratne
Format: Article
Language:English
Published: BMC 2018-11-01
Series:Allergy, Asthma & Clinical Immunology
Subjects:
Online Access:http://link.springer.com/article/10.1186/s13223-018-0292-3