Carbohydrate status in patients with phenylketonuria

Carbohydrate status in patients with phenylketonuria

Abstract Background In patients with phenylketonuria (PKU), a low-phenylalanine (Phe) diet supplemented with low-protein foods and a Phe-free amino acid mixture favors a dietary intake rich in carbohydrates, but little is known about how these molecules are metabolized in this setting. The objective...

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Bibliographic Details
Main Authors: María L. Couce, Paula Sánchez-Pintos, Isidro Vitoria, María-José De Castro, Luís Aldámiz-Echevarría, Patricia Correcher, Ana Fernández-Marmiesse, Iria Roca, Alvaro Hermida, Miguel Martínez-Olmos, Rosaura Leis
Format: Article
Language:English
Published: BMC 2018-06-01
Series:Orphanet Journal of Rare Diseases
Subjects:
HOMA index
Insulin
Nutrition
Phenylalanine
Tetrahydrobiopterin
Online Access:http://link.springer.com/article/10.1186/s13023-018-0847-x

Internet

http://link.springer.com/article/10.1186/s13023-018-0847-x

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