THE DIAGNOSTIC AND CLINICAL VALUE OF DETERMINATION OF α1-ANTITRYPSIN PHENOTYPE IN SYSTEMIC VASCULITIDES
α1-Antitrypsin (α1-AT) deficiency is a common genetic disorder characterized by low serum α1-AT levels and a clinical manifestation of pulmonary emphysema and liver disease. In addition to its classical manifestations, α1-AT deficiency frequently accompanies granulomatosis with polyangiitis (GPA); i...
Main Authors: | , , , , , , , , |
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Format: | Article |
Language: | Russian |
Published: |
IMA-PRESS LLC
2017-04-01
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Series: | Научно-практическая ревматология |
Subjects: | |
Online Access: | https://rsp.mediar-press.net/rsp/article/view/2358 |