THE DIAGNOSTIC AND CLINICAL VALUE OF DETERMINATION OF α1-ANTITRYPSIN PHENOTYPE IN SYSTEMIC VASCULITIDES

α1-Antitrypsin (α1-AT) deficiency is a common genetic disorder characterized by low serum α1-AT levels and a clinical manifestation of pulmonary emphysema and liver disease. In addition to its classical manifestations, α1-AT deficiency frequently accompanies granulomatosis with polyangiitis (GPA); i...

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Main Authors: M. Yu. Pervakova, A. L. Chudinov, S. V. Lapin, I. B. Belyaeva, V. I. Mazurov, T. V. Blinova, E. A. Surkova, V. L. Emanuel, O. V. Inamova
Format: Article
Language:Russian
Published: IMA-PRESS LLC 2017-04-01
Series:Научно-практическая ревматология
Subjects:
Online Access:https://rsp.mediar-press.net/rsp/article/view/2358