Report of Six Cases of Chediak-Higashi Syndrome with Regard to Clinical and Laboratory Findings

Chediak - Higashi Syndrome (CHS) is a rare, primary Immunodeficiency disorder with an autosomal recessive (AR) inheritance and characterized by re¬current infection, partial occulocutaneous albinism and an accelerated phase. In this report we describe clinical and laboratory findings from 6 CHS pa¬t...

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Bibliographic Details
Main Authors: Abolhasan Farhoudi, Zahra Chavoshzadeh, Zahra Pourpak, Mina Izadyar, Mohammad Gharagozlou, Masoud Movahedi, Asghar Aghamohamadi, Bahram Mir saeid Ghazi, Mostafa Moin, Nima Rezaei
Format: Article
Language:English
Published: Tehran University of Medical Sciences 2003-12-01
Series:Iranian Journal of Allergy, Asthma and Immunology
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Online Access:https://ijaai.tums.ac.ir/index.php/ijaai/article/view/55