Anesthetic Management for Pediatric Liver Transplantation in a Patient With Propionic Acidemia: A Case Report

Propionic acidemia is an inborn error of metabolism characterized by accumulation of propionic acid due to deficiency of propionyl-CoA carboxylase. Main stay of treatment focuses on reducing dietary protein. However, orthotropic liver transplantation decreases the frequency of metabolic decompensati...

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Bibliographic Details
Main Authors: Luis I. Rodriguez MD, Erica J. Tainsh MD, Eliane Varga MD, Ana C. Mavarez MD
Format: Article
Language:English
Published: SAGE Publishing 2021-05-01
Series:Journal of Investigative Medicine High Impact Case Reports
Online Access:https://doi.org/10.1177/23247096211015025