Diagnosis and treatment of hereditary angioedema with normal C1-inhibitor level

Hereditary angioedema (HAE) with normal C1-inhibitor level is a rare potentially life-threatening disorder with autosomal dominant inheritance which was first described in 2000. Its clinical presentation is similar to HAE with C1-deficiency. The review is summarized data about its prevalence, mechan...

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Bibliographic Details
Main Authors: A. V. Emelyanov, E. V. Leshenkova, G. A. Kameneva
Format: Article
Language:Russian
Published: "Consilium Medicum" Publishing house 2020-12-01
Series:Терапевтический архив
Subjects:
Online Access:https://ter-arkhiv.ru/0040-3660/article/viewFile/60261/43428