Granulomatous Lymphocytic Interstitial Lung Disease (GLILD) in Common Variable Immunodeficiency (CVID): A Multicenter Retrospective Study of Patients From Italian PID Referral Centers

Background: Granulomatous and Lymphocytic Interstitial Lung Diseases (GLILD) is a severe non-infectious complication of Common Variable Immunodeficiency (CVID), often associated with extrapulmonary involvement. Due to a poorly understood pathogenesis, GLILD diagnosis and management criteria still la...

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Main Authors: Francesco Cinetto, Riccardo Scarpa, Maria Carrabba, Davide Firinu, Vassilios Lougaris, Helena Buso, Giulia Garzi, Sabrina Gianese, Valentina Soccodato, Alessandra Punziano, Gianluca Lagnese, Giulio Tessarin, Giulia Costanzo, Nicholas Landini, Stefania Vio, Maria Pia Bondioni, Dario Consonni, Carolina Marasco, Stefano Del Giacco, Marcello Rattazzi, Angelo Vacca, Alessandro Plebani, Giovanna Fabio, Giuseppe Spadaro, Carlo Agostini, Isabella Quinti, Cinzia Milito
Format: Article
Language:English
Published: Frontiers Media S.A. 2021-03-01
Series:Frontiers in Immunology
Subjects:
Online Access:https://www.frontiersin.org/articles/10.3389/fimmu.2021.627423/full