Hybrid Repair of a Thoraco-abdominal Aortic Aneurysm Associated with Loeys-Dietz Syndrome

Introduction: Loeys-Dietz syndrome (LDS) is a genetic syndrome caused by mutations in transforming growth factor beta receptors (TGFBR) 1 and 2. It can manifest with craniofacial, musculoskeletal, cognitive abnormalities, and vascular pathologies including early onset aortic root aneurysms, extensiv...

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Bibliographic Details
Main Authors: Ahmed A. Naiem, Robert J. Doonan, Oren K. Steinmetz
Format: Article
Language:English
Published: Elsevier 2021-01-01
Series:EJVES Vascular Forum
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2666688X21000174