Hereditary angioedema with C1 inhibitor (C1-INH) deficit: the strength of recognition (51 cases)

Hereditary angioedema (HAE) is a rare autosomal dominant disease due to C1 esterase inhibitor deficiency (C1-INH). The disease is characterized by subcutaneous and submucosal edema in the absence of urticaria due to the accumulation of bradykinin. This descriptive study aimed to evaluate the clinica...

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Bibliographic Details
Main Authors: N.T.M.L. Fragnan, A.L.N. Tolentino, G.B. Borba, A.C. Oliveira, J.A. Simões, S.M.U. Palma, R.N. Constantino-Silva, A.S. Grumach
Format: Article
Language:English
Published: Associação Brasileira de Divulgação Científica 2018-11-01
Series:Brazilian Journal of Medical and Biological Research
Subjects:
Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0100-879X2018001200607&lng=en&tlng=en