Mitochondrial diseases: a review

Mitochondria are organelles responsible for production of mostenergy through oxidative phosphorylation process (OXPHOS). Itcontains a double strand DNA (mitDNA) of about 16,500 bp encodingtwo ribosomal RNAs and 37 mitochondrial proteins. Mutation inmitDNA may result in multisystem syndromes known as...

Full description

Bibliographic Details
Main Authors: Daniel Jarovsky, Pedro Shiozawa, Ulisses Augusto Correia Rosalino, Mirna Duarte Barros
Format: Article
Language:English
Published: Instituto Israelita de Ensino e Pesquisa Albert Einstein 2006-12-01
Series:Einstein (São Paulo)
Subjects:
Online Access:http://www.einstein.br/revista/arquivos/PDF/Einstein_vol4_n4_2006_p343.pdf