Inhibitor in Congenital Factor VII Deficiency; A Rare but Serious Therapeutic Challenge—A Systematic Literature Review

Background: Congenital factor (F) VII deficiency is a rare coagulation factor deficiency with an estimated incidence of 1 per 500,000 individuals. Patients with severe FVII deficiency present a broad range of clinical presentations. Alloimmunization against exogenous FVII, as the main challenge of r...

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Bibliographic Details
Main Authors: Nahid Ramezanpour, Farhad Zaker, Arijit Biswas, Akbar Dorgalaleh
Format: Article
Language:English
Published: MDPI AG 2021-01-01
Series:Journal of Clinical Medicine
Subjects:
Online Access:https://www.mdpi.com/2077-0383/10/2/211