PTEN Hamartoma Tumor Syndrome/Cowden Syndrome: Genomics, Oncogenesis, and Imaging Review for Associated Lesions and Malignancy

<i>PTEN</i> hamartoma tumor syndrome/Cowden syndrome (CS) is a rare autosomal dominant syndrome containing a germline <i>PTEN</i> mutation that leads to the development of multisystem hamartomas and oncogenesis. Benign tumors such as Lhermitte–Duclos disease and malignant tum...

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Bibliographic Details
Main Authors: David D. Dragoo, Ahmed Taher, Vincenzo K. Wong, Ahmed Elsaiey, Nikita Consul, Hagar S. Mahmoud, Bilal Mujtaba, Nir Stanietzky, Khaled M. Elsayes
Format: Article
Language:English
Published: MDPI AG 2021-06-01
Series:Cancers
Subjects:
Online Access:https://www.mdpi.com/2072-6694/13/13/3120