Sirolimus in the treatment of kaposiform lymphangiomatosis
Abstract Background Kaposiform lymphangiomatosis (KLA), which is a new subtype of generalized lymphatic anomaly, is a rare disease with a poor prognosis. Currently, there is no standard treatment due to the poor understanding of KLA. Sirolimus, which is an inhibitor of mammalian target of rapamycin,...
Main Authors: | , , , |
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Format: | Article |
Language: | English |
Published: |
BMC
2021-06-01
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Series: | Orphanet Journal of Rare Diseases |
Subjects: | |
Online Access: | https://doi.org/10.1186/s13023-021-01893-3 |