Hereditary Deficiency of the Second Component of Complement: Early Diagnosis and 21-Year Follow-Up of a Family

Complement deficiencies are rare and often underdiagnosed primary immunodeficiencies that may be associated with invasive bacterial diseases. Serious infections with encapsulated organisms (mainly Streptococcus pneumoniae, but also Neisseria meningitides and Haemophilus influenzae type B) are freque...

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Bibliographic Details
Main Authors: Rosa Maria Dellepiane, Lucia Augusta Baselli, Marco Cazzaniga, Vassilios Lougaris, Paolo Macor, Mara Giordano, Roberta Gualtierotti, Massimo Cugno
Format: Article
Language:English
Published: MDPI AG 2020-03-01
Series:Medicina
Subjects:
Online Access:https://www.mdpi.com/1010-660X/56/3/120