Impaired Mitochondrial and Metabolic Function of Fibroblasts Derived from Patients with Recessive Dystrophic and Junctional Epidermolysis Bullosa
Background: Recessive dystrophic epidermolysis bullosa (RDEB) and junctional EB (JEB) are inherited disorders characterised by fragility and blistering of epithelial tissues leading to pain, pruritus, and adherent scarring. The severity and chronic nature of the resultant skin wounds significantly r...
Main Authors: | Ilona Tietzová, Kirk Twaroski, Cindy Eide, Julie H. Ostrander, Peter A. Crawford, Jakub Tolar |
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Format: | Article |
Language: | English |
Published: |
European Medical Journal
2020-12-01
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Series: | European Medical Journal Dermatology |
Subjects: | |
Online Access: | https://www.emjreviews.com/dermatology/article/impaired-mitochondrial-and-metabolic-function-of-fibroblasts-derived-from-patients-with-recessive-dystrophic-and-junctional-epidermolysis-bullosa/ |
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