Desmoplastic Small Round Cell Tumor: A Review of Main Molecular Abnormalities and Emerging Therapy

Desmoplastic Small Round Cell Tumor: A Review of Main Molecular Abnormalities and Emerging Therapy

Desmoplastic small round cell tumor (DSRCT) is an extremely rare, aggressive sarcoma affecting adolescents and young adults with male predominance. Generally, it originates from the serosal surface of the abdominal cavity. The hallmark characteristic of DSRCT is the EWSR1–WT1 gene fusion. This trans...

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Bibliographic Details
Main Authors: Celso Abdon Mello, Fernando Augusto Batista Campos, Tiago Goss Santos, Maria Leticia Gobo Silva, Giovana Tardin Torrezan, Felipe D’Almeida Costa, Maria Nirvana Formiga, Ulisses Nicolau, Antonio Geraldo Nascimento, Cassia Silva, Maria Paula Curado, Suely Akiko Nakagawa, Ademar Lopes, Samuel Aguiar
Format: Article
Language:English
Published: MDPI AG 2021-01-01
Series:Cancers
Subjects:
desmoplastic small round cell tumor
treatment
prognosis
surgery
radiotherapy
chemotherapy
Online Access:https://www.mdpi.com/2072-6694/13/3/498

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https://www.mdpi.com/2072-6694/13/3/498

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