Anaesthetic management of a child with panthothenate kinase-associated neurodegeneration

Panthothenate kinase-associated neurodegeneration (PKAN) (Hallervorden-Spatz disease) is a rare autosomal recessive chromosomal disorder characterised by progressive neuroaxonal dystrophy. The characteristic features include involuntary movements, rigidity, mental retardation, seizures, emaciation....

Full description

Bibliographic Details
Main Authors: Renu Sinha, Ghansham Biyani, Sulagna Bhattacharjee
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2015-01-01
Series:Indian Journal of Anaesthesia
Subjects:
Online Access:http://www.ijaweb.org/article.asp?issn=0019-5049;year=2015;volume=59;issue=1;spage=43;epage=46;aulast=Sinha