A case of vascular Ehlers–Danlos syndrome with a ruptured hepatic artery after surgical treatment of peritonitis caused by the perforation of the colon

A case of vascular Ehlers–Danlos syndrome with a ruptured hepatic artery after surgical treatment of peritonitis caused by the perforation of the colon

Abstract Background Ehlers–Danlos syndrome (EDS) is an inherited disorder that causes connective tissue fragility. The vascular type of EDS (vEDS) caused by defective collagen type III production accounts for 5%–10% of all EDS cases. Patients can develop gastrointestinal or arterial ruptures, which...

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Bibliographic Details
Main Authors: Daisuke Kakinuma, Takeshi Yamada, Yoshikazu Kanazawa, Kunihiko Matsuno, Tomoko Sahara, Hiroshi Yoshida
Format: Article
Language:English
Published: SpringerOpen 2021-03-01
Series:Surgical Case Reports
Subjects:
Vascular type of Ehlers–Danlos syndrome
Sigmoid colon perforation
Hepatic artery rupture
Pan-peritonitis
Remote vascular catastrophe
Online Access:https://doi.org/10.1186/s40792-021-01156-0

Internet

https://doi.org/10.1186/s40792-021-01156-0

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