The lung in amyloidosis

Amyloidosis is a disorder caused by misfolding of autologous protein and its extracellular deposition as fibrils, resulting in vital organ dysfunction and eventually death. Pulmonary amyloidosis may be localised or part of systemic amyloidosis. Pulmonary interstitial amyloidosis is symptomatic only...

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Bibliographic Details
Main Authors: Paolo Milani, Marco Basset, Francesca Russo, Andrea Foli, Giovanni Palladini, Giampaolo Merlini
Format: Article
Language:English
Published: European Respiratory Society 2017-09-01
Series:European Respiratory Review
Online Access:http://err.ersjournals.com/content/26/145/170046.full