The case of idiopathic pleuroparenchymal fibroelastosis diagnosed by transbronchial biopsy

Pleuroparenchymal fibroelastosis (PPFE) is claasified in idiopathic interstitial pneumonitis group is rarely seen. Etiology and pathophysiology of this entity are not completely understood. The prognosis is poor, and there is no effective treatment except for lung transplantation. Here, we presented...

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Bibliographic Details
Main Authors: Huseyin Arpag, Muhammet Sayan, Nurhan Atilla, Fulsen Bozkus, Hasan Kahraman, Abdulkadir Yasir Bahar, Mahmut Tokur
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2018-01-01
Series:Eurasian Journal of Pulmonology
Subjects:
Online Access:http://www.eurasianjpulmonol.com/article.asp?issn=2148-5402;year=2018;volume=20;issue=2;spage=104;epage=106;aulast=Arpag