Hemophagocytic lymphohistiocytosis of indeterminate cause: a fatal adult case

Hemophagocytic lymphohistiocytosis (HLH) is an uncommon life-threatening disorder characterized by wide spread non-neoplastic proliferation and inappropriate activation of mature macrophages resulting in hypercytokinemia. This uncontrollable and ineffective systemic immune response causes fever, hep...

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Bibliographic Details
Main Authors: Fernando Peixoto Ferraz de Campos, Elizabeth In Myung Kim, Luciana Andréa Avena Smeili, Patrícia Picciarelli de Lima, Fabiana Roberto Lima, Angélica Braz Simões, Maria Claudia Nogueira Zerbini
Format: Article
Language:English
Published: University of São Paulo 2012-06-01
Series:Autopsy and Case Reports
Subjects:
Online Access:http://www.revistas.usp.br/autopsy/article/view/36457