Spectrum of Genetic Autoinflammatory Diseases Presenting with Cutaneous Symptoms

Autoinflammatory diseases comprise a group of chronic disabling entities characterized by inflammation without the presence of infectious agents, auto-antibodies or antigen-specific T-cells. Many autoinflammatory diseases are caused by monogenic defects, which lead to disturbed immune signalling wit...

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Bibliographic Details
Main Authors: Hanna Bonnekoh, Monique Butze, Tilmann Kallinich, Naotomo Kambe, Georgios Kokolakis, Karoline Krause
Format: Article
Language:English
Published: Society for Publication of Acta Dermato-Venereologica 2020-03-01
Series:Acta Dermato-Venereologica
Subjects:
Online Access: https://www.medicaljournals.se/acta/content/html/10.2340/00015555-3427