Adult-onset Langerhans cell histiocytosis presenting with adipsic diabetes insipidus, diabetes mellitus and hypopituitarism: A case report and review of literature

Langerhans cell (LCH) histiocytosis occurs in 1 per 560,000 adults with variable manifestations. However, it rarely presents with simultaneous and multiple endocrine dysfunctions early in the course of the disease. We report a case of LCH in an adult manifesting with adipsic diabetes insipidus, diab...

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Bibliographic Details
Main Authors: Erick S. Mendoza, MD, Amy A. Lopez, MD, Valerie Ann U. Valdez, MD, Jean D. Uy-Ho, MD, Sjoberg A. Kho, MD
Format: Article
Language:English
Published: Elsevier 2015-07-01
Series:Journal of Clinical and Translational Endocrinology Case Reports
Online Access:http://www.sciencedirect.com/science/article/pii/S2214624515000027