Anesthetic management of a patient with congenital insensitivity to pain with anhidrosis by coadministration of remifentanil

Abstract Background Congenital insensitivity to pain with anhidrosis (CIPA) is a rare autosomal recessive disease characterized by unexplained fever, systemic insensitivity to pain, anhidrosis, and mental distress. Anesthetic management is challenging because autonomic dysfunction can induce periope...

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Bibliographic Details
Main Authors: Yoko Takeuchi, Yoshihito Fujita, Takeshi Shimomura, Shuji Kurokawa, Hiroki Noguchi, Yoshihiro Fujiwara
Format: Article
Language:English
Published: SpringerOpen 2018-10-01
Series:JA Clinical Reports
Subjects:
Online Access:http://link.springer.com/article/10.1186/s40981-018-0208-8