Effect of dietary regime on metabolic control in phenylketonuria: Is exact calculation of phenylalanine intake really necessary?

Background: A phenylalanine (Phe) restricted dietary management is required in phenylketonuria (PKU) to maintain good metabolic control. Nevertheless, five different models of dietary regimes, which differ in their accuracy of Phe documentation, are used. To investigate the effect of the dietary reg...

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Main Authors: Carmen Rohde, Alena Gerlinde Thiele, Ulrike Och, Katrin Schönherr, Uta Meyer, Stefanie Rosenbaum-Fabian, Cornelia Maddalon, Sabine Matzken, Holger Blessing, Frauke Lang, Monika Jörg-Streller, Skadi Beblo
Format: Article
Language:English
Published: Elsevier 2015-12-01
Series:Molecular Genetics and Metabolism Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2214426915300343