Anaesthetic management of a patient with Pompe disease for kyphoscoliosis correction

Anaesthetic management of a patient with Pompe disease for kyphoscoliosis correction

Pompe disease (PD) is a type II glycogen storage disease, characterised by abnormal glycogen deposition, mainly in heart and skeletal muscles, leading to progressive loss of muscle function. The infantile variety is associated with severe hypertrophic cardiomyopathy and generally do not reach adulth...

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Bibliographic Details
Main Authors: Vaishali Kumbar, Jayashree Simha, Parameswara Gundappa
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2016-01-01
Series:Indian Journal of Anaesthesia
Subjects:
Anaesthesia
cardiomyopathy
dexmedetomidine
glycogen storage disease
kyphoscoliosis
motor evoked potentials
Pompe disease
Online Access:http://www.ijaweb.org/article.asp?issn=0019-5049;year=2016;volume=60;issue=5;spage=349;epage=351;aulast=Kumbar

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http://www.ijaweb.org/article.asp?issn=0019-5049;year=2016;volume=60;issue=5;spage=349;epage=351;aulast=Kumbar

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