Interstitial lung disease and pre-capillary pulmonary hypertension in neurofibromatosis type 1

Although previously reported, the existence of a neurofibromatosis (NF)-associated diffuse lung disease (DLD) still lacks solid evidence. We report a case of a 68-year-old non-smoking female with NF1, pre-capillary pulmonary hypertension (PH) and an interstitial lung pattern. Initial findings includ...

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Bibliographic Details
Main Authors: Daniela Rodrigues, Hugo Oliveira, Carina Andrade, Luísa Carvalho, Susana Guimarães, Conceição Souto Moura, Ana Paula Vaz
Format: Article
Language:English
Published: Elsevier 2018-01-01
Series:Respiratory Medicine Case Reports
Online Access:http://www.sciencedirect.com/science/article/pii/S2213007117303908