Hemin Augments Growth and Hemoglobinization of Erythroid Precursors from Patients with Diamond-Blackfan Anemia

Diamond-Blackfan anemia (DBA) is congenital pure red-cell anemia due to a differentiation block in erythroid precursors. The disease is commonly caused by mutations in genes for ribosomal proteins. Despite the identification of disease causal genes, the disease pathogenesis is not completely elucida...

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Bibliographic Details
Main Authors: Eitan Fibach, Memet Aker
Format: Article
Language:English
Published: Hindawi Limited 2012-01-01
Series:Anemia
Online Access:http://dx.doi.org/10.1155/2012/940260