When Limb Surgery Has Become the Only Life-Saving Therapy in FOP: A Case Report and Systematic Review of the Literature

Fibrodysplasia ossificans progressiva (FOP) is a rare disease in which heterotopic ossification (HO) is formed in muscles, tendons and ligaments. Traumatic events, including surgery, are discouraged as this is known to trigger a flare-up with risk of subsequent HO. Anesthetic management for patients...

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Main Authors: Esmée Botman, Sanne Treurniet, Wouter D. Lubbers, Lothar A. Schwarte, Patrick R. Schober, Louise Sabelis, Edgar J. G. Peters, Annelies van Schie, Ralph de Vries, Zvi Grunwald, Bernard J. Smilde, Jakko A. Nieuwenhuijzen, Marieke Visser, Dimitra Micha, Nathalie Bravenboer, J. Coen Netelenbos, Bernd P. Teunissen, Pim de Graaf, Pieter G. H. M. Raijmakers, Jan Maerten Smit, Elisabeth M. W. Eekhoff
Format: Article
Language:English
Published: Frontiers Media S.A. 2020-08-01
Series:Frontiers in Endocrinology
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Online Access:https://www.frontiersin.org/article/10.3389/fendo.2020.00570/full