Primary pulmonary lymphangiectasia in Noonan syndrome: apropos of an extremely rare manifestation and a brief literature review
Noonan syndrome (NS) is a genetic multisystem disorder characterised by distinctive facial features, developmental delay, learning difficulties, short stature, congenital heart disease, renal anomalies, bleeding difficulties and lymphatic malformations. Although lymphatic dysplasias are present in...
Main Authors: | , , , |
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Format: | Article |
Language: | English |
Published: |
PAGEPress Publications
2020-12-01
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Series: | Monaldi Archives for Chest Disease |
Subjects: | |
Online Access: | https://monaldi-archives.org/index.php/macd/article/view/1576 |