Extreme hypertriglyceridemia in an infant with hemophagocytic lymphohistiocytosis and hydroxycobalamin deficiency

Introduction. Hemophagocytic lymphohistiocytosis (HLH) is a severe hyperinflammatory condition characterized by fever, cytopenias, hepatosplenomegaly and hemophagocytosis. HLH may be primary or secondary to infection, autoimmune disease or malignancy. Hypertriglyceridemia is a common abn...

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Bibliographic Details
Main Authors: Dokmanović Lidija, Krstovski Nada, Lazić Jelena, Rodić Predrag, Milošević Goran, Janković Srđa, Janić Dragana
Format: Article
Language:English
Published: Serbian Medical Society 2015-01-01
Series:Srpski Arhiv za Celokupno Lekarstvo
Subjects:
Online Access:http://www.doiserbia.nb.rs/img/doi/0370-8179/2015/0370-81791512744D.pdf