Ciliary Videomicroscopy: A Long Beat from the European Respiratory Society Guidelines to the Recognition as a Confirmatory Test for Primary Ciliary Dyskinesia

Primary ciliary dyskinesia (PCD) is a rare inherited ciliopathy in which respiratory cilia are stationary or dyskinetic. The clinical presentation of PCD is highly non-specific since it includes infections and disorders of the upper (otitis and rhinosinusitis) and lower (neonatal respiratory distres...

Full description

Bibliographic Details
Main Authors: Noemie Bricmont, Mihaela Alexandru, Bruno Louis, Jean-François Papon, Céline Kempeneers
Format: Article
Language:English
Published: MDPI AG 2021-09-01
Series:Diagnostics
Subjects:
Online Access:https://www.mdpi.com/2075-4418/11/9/1700