Fatal rupture of pulmonary arteriovenous malformation in hereditary haemorrhagic telangiectasis and severe PAH

Fatal rupture of pulmonary arteriovenous malformation in hereditary haemorrhagic telangiectasis and severe PAH

29-yr-old patient with hereditary haemorrhagic telangiectasia was referred to the present authors’ centre with progressive exertional dyspnoea. Pulmonary arterial hypertension (PAH) was suspected on Doppler echocardiography and confirmed by right heart catheterisation demonstrating severe PAH. Genet...

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Bibliographic Details
Main Authors: D. Montani, L. C. Price, B. Girerd, T. Chinet, P. Lacombe, G. Simonneau, M. Humbert
Format: Article
Language:English
Published: European Respiratory Society 2009-03-01
Series:European Respiratory Review
Subjects:
Activin receptor-like kinase-1
arteriovenous malformation
embolisation
hereditary haemorrhagic telangiectasia
pulmonary arterial hypertension
rupture
Online Access:http://err.ersjournals.com/cgi/content/full/18/111/42

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http://err.ersjournals.com/cgi/content/full/18/111/42

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