Glycomacropeptide: long-term use and impact on blood phenylalanine, growth and nutritional status in children with PKU

Glycomacropeptide: long-term use and impact on blood phenylalanine, growth and nutritional status in children with PKU

Abstract In phenylketonuria, casein glycomacropeptide (CGMP) requires modification with the addition of some essential and semi essential amino acids to ensure suitability as a protein substitute. The optimal amount and ratio of additional amino acids is undefined. Aim A longitudinal, parallel, cont...

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Bibliographic Details
Main Authors: A. Daly, S. Evans, S. Chahal, S. Santra, A. Pinto, R. Jackson, C. Gingell, J. Rocha, F. J. Van Spronsen, A. MacDonald
Format: Article
Language:English
Published: BMC 2019-02-01
Series:Orphanet Journal of Rare Diseases
Subjects:
Glycomacropeptide
Phenylalanine
Large neutral amino acids
Protein substitute
Phenylketonuria
Online Access:http://link.springer.com/article/10.1186/s13023-019-1011-y

Internet

http://link.springer.com/article/10.1186/s13023-019-1011-y

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