Auditory cortex hypoperfusion: a metabolic hallmark in Beta Thalassemia

Abstract Background Sensorineural hearing loss in beta-thalassemia is common and it is generally associated with iron chelation therapy. However, data are scarce, especially on adult populations, and a possible involvement of the central auditory areas has not been investigated yet. We performed a m...

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Bibliographic Details
Main Authors: Renzo Manara, Sara Ponticorvo, Silverio Perrotta, Maria Rosaria Barillari, Giuseppe Costa, Davide Brotto, Rosanna Di Concilio, Angela Ciancio, Elisa De Michele, Pasquale Alessandro Carafa, Antonietta Canna, Andrea Gerardo Russo, Donato Troisi, Martina Caiazza, Federica Ammendola, Domenico Roberti, Claudia Santoro, Stefania Picariello, Maria Sole Valentino, Emanuela Inserra, Roberta Carfora, Mario Cirillo, Simona Raimo, Gabriella Santangelo, Francesco di Salle, Fabrizio Esposito, Immacolata Tartaglione
Format: Article
Language:English
Published: BMC 2021-08-01
Series:Orphanet Journal of Rare Diseases
Subjects:
Online Access:https://doi.org/10.1186/s13023-021-01969-0