Cutaneous Manifestations of Cystic Fibrosis
Cystic fibrosis (CF) is an autosomal recessive affliction triggered by genetic mutations in the cystic fibrosis transmembrane conductance regulator. The lung and pancreas are the most frequently affected organs in cystic fibrosis, cutaneous involvement is undervalued and underdiag-nosed. Skin lesion...
Main Authors: | , , , |
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Format: | Article |
Language: | English |
Published: |
Sciendo
2018-03-01
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Series: | Journal of Interdisciplinary Medicine |
Subjects: | |
Online Access: | https://doi.org/10.2478/jim-2018-0005 |