Survey of actual conditions of erythema marginatum as a prodromal symptom in Japanese patients with hereditary angioedema

Background: Hereditary angioedema (HAE) is a rare but life-threatening condition. HAE types I and II (HAE-1/2) result from C1-inhibitor (C1–INH) deficiency. However, recent genetic analysis has established a new type of HAE with normal C1–INH (HAEnC1-INH). The mutations of factor XII, plasminogen, a...

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Bibliographic Details
Main Authors: Isao Ohsawa, Atsushi Fukunaga, Shinya Imamura, Kazumasa Iwamoto, Akio Tanaka, Michihiro Hide, Daisuke Honda, Kouhei Yamashita, Chisako Fujiwara, Osamu Ishikawa, Takeo Yamaguchi, Junichi Maehara, Tomoya Hirose, Masahiro Ieko, Kunihiko Umekita, Yuya Nakamura, Hiromichi Gotoh
Format: Article
Language:English
Published: Elsevier 2021-02-01
Series:World Allergy Organization Journal
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Online Access:http://www.sciencedirect.com/science/article/pii/S1939455121000053