Linear scleroderma “en coup de sabre” with extensive brain involvement—Clinicopathologic correlations and response to anti-Interleukin-6 therapy

Linear scleroderma “en coup de sabre” with extensive brain involvement—Clinicopathologic correlations and response to anti-Interleukin-6 therapy

Abstract Linear scleroderma “en coup de sabre” (LSES) variant is a cephalic subtype of localized scleroderma that can be associated with extracutaneous stigmata, such as epilepsy, dementia syndromes, as well as focal central nervous system neurologic deficits. While the pathophysiology of cutaneous...

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Bibliographic Details
Main Authors: Cynthia M. Magro, Pierre Halteh, Luke C. Olson, Ilya Kister, Lee Shapiro
Format: Article
Language:English
Published: BMC 2019-05-01
Series:Orphanet Journal of Rare Diseases
Subjects:
Linear scleroderma
“en coupe de sabre,” vasculitis
Autoimmune endotheliopathy
Online Access:http://link.springer.com/article/10.1186/s13023-019-1015-7

Internet

http://link.springer.com/article/10.1186/s13023-019-1015-7

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