Linear scleroderma “en coup de sabre” with extensive brain involvement—Clinicopathologic correlations and response to anti-Interleukin-6 therapy
Abstract Linear scleroderma “en coup de sabre” (LSES) variant is a cephalic subtype of localized scleroderma that can be associated with extracutaneous stigmata, such as epilepsy, dementia syndromes, as well as focal central nervous system neurologic deficits. While the pathophysiology of cutaneous...
Main Authors: | Cynthia M. Magro, Pierre Halteh, Luke C. Olson, Ilya Kister, Lee Shapiro |
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Format: | Article |
Language: | English |
Published: |
BMC
2019-05-01
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Series: | Orphanet Journal of Rare Diseases |
Subjects: | |
Online Access: | http://link.springer.com/article/10.1186/s13023-019-1015-7 |
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