Radiological pleuroparenchymal fibroelastosis associated to limited cutaneous systemic sclerosis: a case report

Radiological pleuroparenchymal fibroelastosis associated to limited cutaneous systemic sclerosis: a case report

Abstract Background Pleuroparenchymal fibroelastosis (PPFE) is a very rare interstitial lung disease (ILD) characterized by progressive fibrotic lesions of the visceral pleura and the sub-pleural parenchyma, affecting predominantly the upper lobes. PPFE may occur in different contextes like bone mar...

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Bibliographic Details
Main Authors: D. Hassoun, S. Dirou, P. P. Arrigoni, C. Durant, M. Hamidou, A. Néel, C. Agard
Format: Article
Language:English
Published: BMC 2018-05-01
Series:BMC Pulmonary Medicine
Subjects:
Pleuroparenchymal fibroelastosis
Systemic sclerosis
Interstitial lung disease
Online Access:http://link.springer.com/article/10.1186/s12890-018-0641-5

Internet

http://link.springer.com/article/10.1186/s12890-018-0641-5

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