Dietary management of maternal phenylketonuria with glycomacropeptide and amino acids supplements: A case report

Dietary management of maternal phenylketonuria with glycomacropeptide and amino acids supplements: A case report

Background: In maternal PKU, protein substitute (PS) is provided by phenylalanine (PHE)-free l-amino acids (AA), but glycomacropeptide-based protein substitute (GMP) is an alternative consideration. Objective: To describe the first Portuguese Maternal Phenylketonuria (MPKU) partially managed with GM...

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Bibliographic Details
Main Authors: A. Pinto, M.F. Almeida, A. Cunha, C. Carmona, S. Rocha, A. Guimas, R. Ribeiro, C.R. Mota, E. Martins, A. MacDonald, J.C. Rocha
Format: Article
Language:English
Published: Elsevier 2017-12-01
Series:Molecular Genetics and Metabolism Reports
Subjects:
Maternal phenylketonuria
Glycomacropeptide
l-Amino acids
Phenylalanine
Tyrosine
Online Access:http://www.sciencedirect.com/science/article/pii/S2214426917301222

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http://www.sciencedirect.com/science/article/pii/S2214426917301222

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