A proposed prognostic prediction score for pleuroparenchymal fibroelastosis

Abstract Background Clinical course of pleuroparenchymal fibroelastosis (PPFE) shows considerable variation among patients, but there is no established prognostic prediction model for PPFE. Methods The prediction model was developed using retrospective data from two cohorts: our single-center cohort...

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Bibliographic Details
Main Authors: Yoshiaki Kinoshita, Takato Ikeda, Takuto Miyamura, Yusuke Ueda, Yuji Yoshida, Hisako Kushima, Masaki Fujita, Takashi Ogura, Kentaro Watanabe, Hiroshi Ishii
Format: Article
Language:English
Published: BMC 2021-07-01
Series:Respiratory Research
Subjects:
Online Access:https://doi.org/10.1186/s12931-021-01810-z